Incontinentia pigmenti: A propósito de un caso

Incontinentia pigmenti: A propósito de un caso.
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Incontinentia pigmenti: A propósito de un caso.

Incontinentia Pigmenti is a rare X-linked multisystem neuroectodermic disorder with signs and symptoms related mainly to the dermatologic, dental, ocular and central nervous systems, and characterized by death in the majority of male embryos. Affected children do not appear sick, in spite of the ski...

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Journal Title: Revista Medica Herediana
Main Author: Tori Tori Carlos
Other Authors: Enriqueta Villar De Cipriani;
Javier Arias Stella;
Carmen Avalos
Language: Spanish
Get full text: http://www.upch.edu.pe/vrinve/dugic/revistas/index.php/RMH/article/view/487
Resource type: Journal article
Source: Revista Medica Herediana; Vol 6, No 3 (Year 1995).
DOI: http://dx.doi.org/10.20453/rmh.v6i3.487
Publisher: Universidad Peruana Cayetano Heredia
Usage rights: Reconocimiento (by)
Subjects: Applied Sciences --> Medicine, General & Internal
Abstract: Incontinentia Pigmenti is a rare X-linked multisystem neuroectodermic disorder with signs and symptoms related mainly to the dermatologic, dental, ocular and central nervous systems, and characterized by death in the majority of male embryos. Affected children do not appear sick, in spite of the skin eruption, the peripheral leucocytosis and marked eosinophilia. Most of the cases are reported in caucasians, although there are description in black children, orientals, north central and south american Indians, and in our mestizos. The name of Incontinentia Pigmenti describes the incontinence of the melanin pigment from the basal layer of the epidemermis into the superficial dermis.